This disorder is characterized by progressive cerebellar atrophy,
peripheral neuropathy, Oculomotor apraxia in ∼50% of the patients and elevated α-fetoprotein levels with an age of onset between 10 and 20 years.
Clinically, this type of convulsions is manifested by focal clonic or generalized multifocal epiprips, characterized by short periods of respiratory arrest,
stereotypical motor phenomena and Oculomotor phenomena of the type of tonic tension of the muscles along the spine,
tonic reflexes.